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Craniovertebral Junction Meningocele: A Case Report


Background: Spina bifida is a congenital abnormality in neural tube that frequently occurs in the lumbosacral region and rarely occurs in the cervical region. Abnormality of the neural tube is one of the most common congenital disorders in the worldwide, with a prevalence ranging from 0.5 to more than 10 per 1,000 pregnancies. Meningocele at the cervical junction is a very rare congenital disorder. Our knowledge of this condition is very limited due to small retrospective case series and the limited number of case reports.

Case presentation: A 4-month-old boy with a mass in craniovertebral area covered with normal skin, measuring 6 cm in diameter, with semi-solid consistency. The CT scan of the head found hydrocephalus and type 1 Chiari malformation accompanied by fluid-filled cysts in the subcutaneous tissue in the craniovertebral area which has consistent findings with meningocele. The patients underwent Ventriculoperitoneal shunt and surgical excision to repair the meningocele. Postoperatively, no complications occurred and reported during both procedures, and the patient had no additional deficits.

Conclusion: Meningocele at the craniovertebral junction remains a rare case of congenital abnormalities. A comprehensive excisional operation is the first choice, and resulted in satisfactory outcome. Although there were no neurological abnormalities, we need to perform surgery as early as possible in these cases to prevent the occurrence of neurological disorders in the future.

Keywords: Chiari malformation, craniovertebral junction, hydrocephalus, meningocele, spina bifida


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How to Cite

Pahlevi, F. R., Heryani, D., & Ma’ruf, A. Z. (2019). Craniovertebral Junction Meningocele: A Case Report. Indonesian Journal of Neurosurgery, 2(3).




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Faizal Reza Pahlevi
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Dini Heryani
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Achmad Zuhro Ma'ruf
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